Click here ► https://sites.google.com/site/foodsafetypolicy/comment-variant-cjd-in-second-genetic-type to find out more. #bse #cjd #food #safety Joe Crowley's (the presenter's) filming diary () For me and friends of my age, Mad Cow Disease seems like a distant nightmare - something that haunted us on the news as we grew up. But this Inside Out programme has made me think again and, sadly, given the disease a painful new relevance. It's about a young guy like me, starting out on a career in the media, when he was struck down by the human form of the disease. And it's a story of his mother's (Christine Lord) relentless search for answers, as she tries to find out who killed her son (Andrew Black). Further informarion on variant CJD Inside Out looks at the rise of Variant CJD, the symptoms and the support available for those caring for or mourning the loss of loved ones from the disease. Variant CJD Variant CJD is a form of transmissible dementia and differs from other forms of CJD. It has received a lot of media attention over recent years, but has been around for much longer. Early 1920s CJD is first recognised by two German neurologists Creuzfeldt and Jakob, the namesakes of the disease. Following decades It is a rare disease with an estimated UK occurrence of 30-50 cases per year. Dec 1984 Cow number 133 on Stent farm Sussex becomes the first confirmed victim of BSE the animal strain of CJD. Feb 1985 Cow 133 dies. Nov 1986 BSE is first formally identified by the Central Veterinary Laboratory. April 1988 The Government establishes the Southwood committee to look into BSE. It concludes that BSE is probably spread in animal feed. May 1990 Chief Medical Officer says beef is safe to eat. July 1993 100,000th case of BSE in Britain. May 1995 First death from Variant CJD. March 1996 Government announces suspected link between BSE and the human equivalent CJD . The EU announces worldwide export ban on all British beef. March 1998 A public inquiry into the origin and spread of BSE and CJD opens in London. Jan 2000 Claire Mcvey, age 15, dies of Variant CJD. August 2002 92 deaths in Britain to date from definite Variant CJD . 22 deaths from probable Variant CJD. Symptoms Although symptoms are diverse across patients, a number of similarities have been found when sufferers' brain were examined under a microscope. According to the Crentzfelt-Jakob Support Network, most had lost nerve cells in the brain leading to a spongy appearance. There are many symptoms of Variant CJD, which can broadly be split into two categories... Physical symptoms: Unsteadiness on feet Development of uncontrollable jerky movements Progressive stiffness of the limbs Incontinence Mental symptoms: The progressive loss of mental abilities Mood swings Loss of awareness of surroundings The incubation period for the disease is years rather than weeks or months. Therefore, the symptoms get progressively worse over time. Medicine According to the Crentzfelt-Jakob Support Network, most people with CJD die within six months. But in about 10 per cent of cases it can last between two and five years. At present, there is no known cure for CJD despite considerable, ongoing research. There are some medicines which make the last few weeks easier for sufferers. Source of information: http://www.bbc.co.uk/insideout/southwest/series1/claire-mcvey.shtml Bovine spongiform encephalopathy (BSE), commonly known as mad cow disease, is a neurodegenerative disease of cattle. Symptoms include abnormal behavior, trouble walking, and weight loss.Later in the course of the disease the cow becomes unable to move. The time between infection and onset of symptoms is generally four to five years. Time from onset of symptoms to death is generally weeks to months. Spread to humans is believed to result in variant Creutzfeldt–Jakob disease (vCJD). As of 2018, a total of 231 cases of vCJD have been reported globally. BSE is thought to be due to an infection by a misfolded protein, known as a prion. Cattle are believed to have been infected by being fed meat-and-bone meal (MBM) that contained the remains of cattle who spontaneously developed the disease or scrapie-infected sheep products. The outbreak increased throughout the United Kingdom due to the practice of feeding meat-and-bone meal to young calves of dairy cows. Cases are suspected based on symptoms and confirmed by examination of the brain. Cases are classified as classic or atypical, with the latter divided into H- and L types. It is a type of transmissible spongiform encephalopathy (TSE). Efforts to prevent the disease in the UK include not allowing any animal older than 30 months to enter either the human food or animal feed supply. In Europe all cattle over 30 months must be tested if they will become human food. In North America tissue of concern, known as specified risk material, may not be added to animal feed or pet food.

• published: 02 Jul 2010
• views: 8200